mitochondrion organization Gene Set

Dataset GO Biological Process Annotations
Category structural or functional annotations
Type biological process
Description A process that is carried out at the cellular level which results in the assembly, arrangement of constituent parts, or disassembly of a mitochondrion; includes mitochondrial morphogenesis and distribution, and replication of the mitochondrial genome as well as synthesis of new mitochondrial components. (Gene Ontology, GO_0007005)
External Link http://amigo.geneontology.org/amigo/term/GO:0007005
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Genes

313 genes participating in the mitochondrion organization biological process from the curated GO Biological Process Annotations dataset.

Symbol Name
ACAA2 acetyl-CoA acyltransferase 2
AFG3L2 AFG3-like AAA ATPase 2
AGTPBP1 ATP/GTP binding protein 1
AIFM2 apoptosis-inducing factor, mitochondrion-associated, 2
AKT1 v-akt murine thymoma viral oncogene homolog 1
AKT3 v-akt murine thymoma viral oncogene homolog 3
ALAS1 5'-aminolevulinate synthase 1
ALKBH7 alkB, alkylation repair homolog 7 (E. coli)
ATCAY ataxia, cerebellar, Cayman type
ATF2 activating transcription factor 2
ATG12 autophagy related 12
ATG2A autophagy related 2A
ATG2B autophagy related 2B
ATG3 autophagy related 3
ATG4A autophagy related 4A, cysteine peptidase
ATG4B autophagy related 4B, cysteine peptidase
ATG4C autophagy related 4C, cysteine peptidase
ATG4D autophagy related 4D, cysteine peptidase
ATG5 autophagy related 5
ATG7 autophagy related 7
ATG9A autophagy related 9A
ATP2A1 ATPase, Ca++ transporting, cardiac muscle, fast twitch 1
ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide
ATP7A ATPase, Cu++ transporting, alpha polypeptide
AURKAIP1 aurora kinase A interacting protein 1
BAD BCL2-associated agonist of cell death
BAK1 BCL2-antagonist/killer 1
BAX BCL2-associated X protein
BCL2 B-cell CLL/lymphoma 2
BCL2L1 BCL2-like 1
BCL2L11 BCL2-like 11 (apoptosis facilitator)
BCS1L BC1 (ubiquinol-cytochrome c reductase) synthesis-like
BHLHA15 basic helix-loop-helix family, member a15
BID BH3 interacting domain death agonist
BIK BCL2-interacting killer (apoptosis-inducing)
BLOC1S2 biogenesis of lysosomal organelles complex-1, subunit 2
BNIP3 BCL2/adenovirus E1B 19kDa interacting protein 3
BNIP3L BCL2/adenovirus E1B 19kDa interacting protein 3-like
C10ORF2 chromosome 10 open reading frame 2
C22ORF29 chromosome 22 open reading frame 29
CAMK2A calcium/calmodulin-dependent protein kinase II alpha
CAMK4 calcium/calmodulin-dependent protein kinase IV
CASP3 caspase 3, apoptosis-related cysteine peptidase
CAV2 caveolin 2
CCAR2 cell cycle and apoptosis regulator 2
CCK cholecystokinin
CEBPA CCAAT/enhancer binding protein (C/EBP), alpha
CHCHD1 coiled-coil-helix-coiled-coil-helix domain containing 1
CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10
CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3
CHCHD6 coiled-coil-helix-coiled-coil-helix domain containing 6
CISD2 CDGSH iron sulfur domain 2
CLN8 ceroid-lipofuscinosis, neuronal 8 (epilepsy, progressive with mental retardation)
CLU clusterin
CLUH clustered mitochondria (cluA/CLU1) homolog
CNP 2',3'-cyclic nucleotide 3' phosphodiesterase
COL4A3BP collagen, type IV, alpha 3 (Goodpasture antigen) binding protein
COQ7 coenzyme Q7 homolog, ubiquinone (yeast)
COX10 COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
COX18 COX18 cytochrome c oxidase assembly factor
CREB1 cAMP responsive element binding protein 1
CXADR coxsackie virus and adenovirus receptor
CYCS cytochrome c, somatic
DAP3 death associated protein 3
DNAJA3 DnaJ (Hsp40) homolog, subfamily A, member 3
DNM1L dynamin 1-like
ELAC2 elaC ribonuclease Z 2
EPAS1 endothelial PAS domain protein 1
ERBB4 erb-b2 receptor tyrosine kinase 4
ESRRA estrogen-related receptor alpha
EYA2 EYA transcriptional coactivator and phosphatase 2
FANCG Fanconi anemia, complementation group G
FBXO7 F-box protein 7
FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae)
FUNDC1 FUN14 domain containing 1
FUNDC2 FUN14 domain containing 2
FXN frataxin
GABARAP GABA(A) receptor-associated protein
GABARAPL1 GABA(A) receptor-associated protein like 1
GABARAPL2 GABA(A) receptor-associated protein-like 2
GABPA GA binding protein transcription factor, alpha subunit 60kDa
GABPB1 GA binding protein transcription factor, beta subunit 1
GADD45GIP1 growth arrest and DNA-damage-inducible, gamma interacting protein 1
GATB glutamyl-tRNA(Gln) amidotransferase, subunit B
GATC glutamyl-tRNA(Gln) amidotransferase, subunit C
GCLC glutamate-cysteine ligase, catalytic subunit
GCLM glutamate-cysteine ligase, modifier subunit
GDAP1 ganglioside induced differentiation associated protein 1
GFM1 G elongation factor, mitochondrial 1
GFM2 G elongation factor, mitochondrial 2
GGCT gamma-glutamylcyclotransferase
HCFC1 host cell factor C1
HEBP2 heme binding protein 2
HK2 hexokinase 2
HMGCL 3-hydroxymethyl-3-methylglutaryl-CoA lyase
HSP90AA1 heat shock protein 90kDa alpha (cytosolic), class A member 1
HSPA4 heat shock 70kDa protein 4
HTRA2 HtrA serine peptidase 2
HTT huntingtin
IARS2 isoleucyl-tRNA synthetase 2, mitochondrial
ICT1 immature colon carcinoma transcript 1
IFI6 interferon, alpha-inducible protein 6
IFIT2 interferon-induced protein with tetratricopeptide repeats 2
JTB jumping translocation breakpoint
JUN jun proto-oncogene
LETM1 leucine zipper-EF-hand containing transmembrane protein 1
LONP1 lon peptidase 1, mitochondrial
LPIN1 lipin 1
LRRK2 leucine-rich repeat kinase 2
MAN2A1 mannosidase, alpha, class 2A, member 1
MAP1LC3A microtubule-associated protein 1 light chain 3 alpha
MAP1LC3B microtubule-associated protein 1 light chain 3 beta
MAP1LC3B2 microtubule-associated protein 1 light chain 3 beta 2
MAP1LC3C microtubule-associated protein 1 light chain 3 gamma
MAP3K1 mitogen-activated protein kinase kinase kinase 1, E3 ubiquitin protein ligase
MAPK11 mitogen-activated protein kinase 11
MAPK12 mitogen-activated protein kinase 12
MAPK14 mitogen-activated protein kinase 14
MAPK9 mitogen-activated protein kinase 9
MARK2 MAP/microtubule affinity-regulating kinase 2
MCL1 myeloid cell leukemia 1
MEF2A myocyte enhancer factor 2A
MFF mitochondrial fission factor
MFN1 mitofusin 1
MFN2 mitofusin 2
MGME1 mitochondrial genome maintenance exonuclease 1
MIEF1 mitochondrial elongation factor 1
MIEF2 mitochondrial elongation factor 2
MOAP1 modulator of apoptosis 1
MPV17 MpV17 mitochondrial inner membrane protein
MRPL1 mitochondrial ribosomal protein L1
MRPL10 mitochondrial ribosomal protein L10
MRPL11 mitochondrial ribosomal protein L11
MRPL12 mitochondrial ribosomal protein L12
MRPL13 mitochondrial ribosomal protein L13
MRPL14 mitochondrial ribosomal protein L14
MRPL15 mitochondrial ribosomal protein L15
MRPL16 mitochondrial ribosomal protein L16
MRPL17 mitochondrial ribosomal protein L17
MRPL18 mitochondrial ribosomal protein L18
MRPL19 mitochondrial ribosomal protein L19
MRPL2 mitochondrial ribosomal protein L2
MRPL20 mitochondrial ribosomal protein L20
MRPL21 mitochondrial ribosomal protein L21
MRPL22 mitochondrial ribosomal protein L22
MRPL23 mitochondrial ribosomal protein L23
MRPL24 mitochondrial ribosomal protein L24
MRPL27 mitochondrial ribosomal protein L27
MRPL28 mitochondrial ribosomal protein L28
MRPL3 mitochondrial ribosomal protein L3
MRPL30 mitochondrial ribosomal protein L30
MRPL32 mitochondrial ribosomal protein L32
MRPL33 mitochondrial ribosomal protein L33
MRPL34 mitochondrial ribosomal protein L34
MRPL35 mitochondrial ribosomal protein L35
MRPL36 mitochondrial ribosomal protein L36
MRPL37 mitochondrial ribosomal protein L37
MRPL38 mitochondrial ribosomal protein L38
MRPL39 mitochondrial ribosomal protein L39
MRPL4 mitochondrial ribosomal protein L4
MRPL40 mitochondrial ribosomal protein L40
MRPL41 mitochondrial ribosomal protein L41
MRPL42 mitochondrial ribosomal protein L42
MRPL43 mitochondrial ribosomal protein L43
MRPL44 mitochondrial ribosomal protein L44
MRPL46 mitochondrial ribosomal protein L46
MRPL47 mitochondrial ribosomal protein L47
MRPL48 mitochondrial ribosomal protein L48
MRPL49 mitochondrial ribosomal protein L49
MRPL50 mitochondrial ribosomal protein L50
MRPL51 mitochondrial ribosomal protein L51
MRPL52 mitochondrial ribosomal protein L52
MRPL53 mitochondrial ribosomal protein L53
MRPL54 mitochondrial ribosomal protein L54
MRPL55 mitochondrial ribosomal protein L55
MRPL9 mitochondrial ribosomal protein L9
MRPS10 mitochondrial ribosomal protein S10
MRPS11 mitochondrial ribosomal protein S11
MRPS12 mitochondrial ribosomal protein S12
MRPS14 mitochondrial ribosomal protein S14
MRPS15 mitochondrial ribosomal protein S15
MRPS16 mitochondrial ribosomal protein S16
MRPS17 mitochondrial ribosomal protein S17
MRPS18A mitochondrial ribosomal protein S18A
MRPS18B mitochondrial ribosomal protein S18B
MRPS18C mitochondrial ribosomal protein S18C
MRPS21 mitochondrial ribosomal protein S21
MRPS22 mitochondrial ribosomal protein S22
MRPS23 mitochondrial ribosomal protein S23
MRPS24 mitochondrial ribosomal protein S24
MRPS25 mitochondrial ribosomal protein S25
MRPS26 mitochondrial ribosomal protein S26
MRPS27 mitochondrial ribosomal protein S27
MRPS28 mitochondrial ribosomal protein S28
MRPS30 mitochondrial ribosomal protein S30
MRPS31 mitochondrial ribosomal protein S31
MRPS33 mitochondrial ribosomal protein S33
MRPS34 mitochondrial ribosomal protein S34
MRPS35 mitochondrial ribosomal protein S35
MRPS36 mitochondrial ribosomal protein S36
MRPS5 mitochondrial ribosomal protein S5
MRPS6 mitochondrial ribosomal protein S6
MRPS7 mitochondrial ribosomal protein S7
MRPS9 mitochondrial ribosomal protein S9
MRRF mitochondrial ribosome recycling factor
MSTO1 misato 1, mitochondrial distribution and morphology regulator
MTCH2 mitochondrial carrier 2
MTERF1 mitochondrial transcription termination factor 1
MTERF4 mitochondrial transcription termination factor 4
MTFMT mitochondrial methionyl-tRNA formyltransferase
MTFP1 mitochondrial fission process 1
MTFR1 mitochondrial fission regulator 1
MTFR2 mitochondrial fission regulator 2
MTIF2 mitochondrial translational initiation factor 2
MTIF3 mitochondrial translational initiation factor 3
MTM1 myotubularin 1
MTO1 mitochondrial tRNA translation optimization 1
MTRF1L mitochondrial translational release factor 1-like
MUL1 mitochondrial E3 ubiquitin protein ligase 1
MYH14 myosin, heavy chain 14, non-muscle
NAIF1 nuclear apoptosis inducing factor 1
NDUFA13 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)
NOA1 nitric oxide associated 1
NOS3 nitric oxide synthase 3 (endothelial cell)
NPTX1 neuronal pentraxin I
NRF1 nuclear respiratory factor 1
NUBPL nucleotide binding protein-like
OMA1 OMA1 zinc metallopeptidase
OPA1 optic atrophy 1 (autosomal dominant)
OPA3 optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia)
P2RX7 purinergic receptor P2X, ligand gated ion channel, 7
PANK2 pantothenate kinase 2
PARK2 parkin RBR E3 ubiquitin protein ligase
PARK7 parkinson protein 7
PID1 phosphotyrosine interaction domain containing 1
PIF1 PIF1 5'-to-3' DNA helicase
PIM2 Pim-2 proto-oncogene, serine/threonine kinase
PINK1 PTEN induced putative kinase 1
PLD6 phospholipase D family, member 6
PMAIP1 phorbol-12-myristate-13-acetate-induced protein 1
PNPT1 polyribonucleotide nucleotidyltransferase 1
POLDIP2 polymerase (DNA-directed), delta interacting protein 2
POLG2 polymerase (DNA directed), gamma 2, accessory subunit
POLRMT polymerase (RNA) mitochondrial (DNA directed)
PPARGC1A peroxisome proliferator-activated receptor gamma, coactivator 1 alpha
PPARGC1B peroxisome proliferator-activated receptor gamma, coactivator 1 beta
PPIF peptidylprolyl isomerase F
PPP2CB protein phosphatase 2, catalytic subunit, beta isozyme
PPRC1 peroxisome proliferator-activated receptor gamma, coactivator-related 1
PRDX3 peroxiredoxin 3
PRKAA2 protein kinase, AMP-activated, alpha 2 catalytic subunit
PRKAB1 protein kinase, AMP-activated, beta 1 non-catalytic subunit
PRKAB2 protein kinase, AMP-activated, beta 2 non-catalytic subunit
PRKAG1 protein kinase, AMP-activated, gamma 1 non-catalytic subunit
PRKAG2 protein kinase, AMP-activated, gamma 2 non-catalytic subunit
PRKAG3 protein kinase, AMP-activated, gamma 3 non-catalytic subunit
PTCD2 pentatricopeptide repeat domain 2
PTCD3 pentatricopeptide repeat domain 3
PTRH1 peptidyl-tRNA hydrolase 1 homolog (S. cerevisiae)
PVRL2 poliovirus receptor-related 2 (herpesvirus entry mediator B)
QRSL1 glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1
RAB3A RAB3A, member RAS oncogene family
RARS2 arginyl-tRNA synthetase 2, mitochondrial
RHOT1 ras homolog family member T1
RHOT2 ras homolog family member T2
SAMM50 SAMM50 sorting and assembly machinery component
SEPT4 septin 4
SFN stratifin
SHARPIN SHANK-associated RH domain interactor
SIRT3 sirtuin 3
SLC25A33 solute carrier family 25 (pyrimidine nucleotide carrier), member 33
SLC25A36 solute carrier family 25 (pyrimidine nucleotide carrier), member 36
SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
SLC4A5 solute carrier family 4 (sodium bicarbonate cotransporter), member 5
SLC9A1 solute carrier family 9, subfamily A (NHE1, cation proton antiporter 1), member 1
SLIRP SRA stem-loop interacting RNA binding protein
SNCA synuclein, alpha (non A4 component of amyloid precursor)
SOD2 superoxide dismutase 2, mitochondrial
SPATA18 spermatogenesis associated 18
SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive)
SQSTM1 sequestosome 1
SSBP1 single-stranded DNA binding protein 1, mitochondrial
STOML2 stomatin (EPB72)-like 2
SUPV3L1 suppressor of var1, 3-like 1 (S. cerevisiae)
SYNJ2BP synaptojanin 2 binding protein
TAZ tafazzin
TEFM transcription elongation factor, mitochondrial
TERT telomerase reverse transcriptase
TFAM transcription factor A, mitochondrial
TFB1M transcription factor B1, mitochondrial
TFB2M transcription factor B2, mitochondrial
THEM4 thioesterase superfamily member 4
TIMM10 translocase of inner mitochondrial membrane 10 homolog (yeast)
TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast)
TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
TIMM9 translocase of inner mitochondrial membrane 9 homolog (yeast)
TMEM11 transmembrane protein 11
TOMM22 translocase of outer mitochondrial membrane 22 homolog (yeast)
TP53 tumor protein p53
TP73 tumor protein p73
TRMT10C tRNA methyltransferase 10 homolog C (S. cerevisiae)
TRMT61B tRNA methyltransferase 61B
TSFM Ts translation elongation factor, mitochondrial
TUFM Tu translation elongation factor, mitochondrial
TYMP thymidine phosphorylase
USP30 ubiquitin specific peptidase 30
WDR45 WD repeat domain 45
WDR45B WD repeat domain 45B
WIPI1 WD repeat domain, phosphoinositide interacting 1
WIPI2 WD repeat domain, phosphoinositide interacting 2
YME1L1 YME1-like 1 ATPase