mitochondrial part Gene Set

Dataset GO Cellular Component Annotations
Category structural or functional annotations
Type cellular component
Description Any constituent part of a mitochondrion, a semiautonomous, self replicating organelle that occurs in varying numbers, shapes, and sizes in the cytoplasm of virtually all eukaryotic cells. It is notably the site of tissue respiration. (Gene Ontology, GO_0044429)
External Link http://amigo.geneontology.org/amigo/term/GO:0044429
Similar Terms
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Genes

868 proteins localized to the mitochondrial part cellular component from the curated GO Cellular Component Annotations dataset.

Symbol Name
AADAT aminoadipate aminotransferase
AASS aminoadipate-semialdehyde synthase
ABAT 4-aminobutyrate aminotransferase
ABCA12 ATP-binding cassette, sub-family A (ABC1), member 12
ABCA8 ATP-binding cassette, sub-family A (ABC1), member 8
ABCB10 ATP-binding cassette, sub-family B (MDR/TAP), member 10
ABCB6 ATP-binding cassette, sub-family B (MDR/TAP), member 6 (Langereis blood group)
ABCB7 ATP-binding cassette, sub-family B (MDR/TAP), member 7
ABCB8 ATP-binding cassette, sub-family B (MDR/TAP), member 8
ABCD3 ATP-binding cassette, sub-family D (ALD), member 3
ABCF2 ATP-binding cassette, sub-family F (GCN20), member 2
ABCG2 ATP-binding cassette, sub-family G (WHITE), member 2 (Junior blood group)
ACAA2 acetyl-CoA acyltransferase 2
ACACB acetyl-CoA carboxylase beta
ACAD11 acyl-CoA dehydrogenase family, member 11
ACAD8 acyl-CoA dehydrogenase family, member 8
ACADL acyl-CoA dehydrogenase, long chain
ACADM acyl-CoA dehydrogenase, C-4 to C-12 straight chain
ACADS acyl-CoA dehydrogenase, C-2 to C-3 short chain
ACADSB acyl-CoA dehydrogenase, short/branched chain
ACADVL acyl-CoA dehydrogenase, very long chain
ACAT1 acetyl-CoA acetyltransferase 1
ACO2 aconitase 2, mitochondrial
ACSL1 acyl-CoA synthetase long-chain family member 1
ACSL3 acyl-CoA synthetase long-chain family member 3
ACSL4 acyl-CoA synthetase long-chain family member 4
ACSL5 acyl-CoA synthetase long-chain family member 5
ACSL6 acyl-CoA synthetase long-chain family member 6
ACSM1 acyl-CoA synthetase medium-chain family member 1
ACSM2A acyl-CoA synthetase medium-chain family member 2A
ACSM2B acyl-CoA synthetase medium-chain family member 2B
ACSM3 acyl-CoA synthetase medium-chain family member 3
ACSM4 acyl-CoA synthetase medium-chain family member 4
ACSM5 acyl-CoA synthetase medium-chain family member 5
ACSS1 acyl-CoA synthetase short-chain family member 1
ADAP2 ArfGAP with dual PH domains 2
ADCK4 aarF domain containing kinase 4
ADHFE1 alcohol dehydrogenase, iron containing, 1
ADPRHL2 ADP-ribosylhydrolase like 2
AFG3L2 AFG3-like AAA ATPase 2
AGK acylglycerol kinase
AGPAT5 1-acylglycerol-3-phosphate O-acyltransferase 5
AGXT alanine-glyoxylate aminotransferase
AGXT2 alanine--glyoxylate aminotransferase 2
AIFM1 apoptosis-inducing factor, mitochondrion-associated, 1
AIFM2 apoptosis-inducing factor, mitochondrion-associated, 2
AIFM3 apoptosis-inducing factor, mitochondrion-associated, 3
AK2 adenylate kinase 2
AK3 adenylate kinase 3
AKAP1 A kinase (PRKA) anchor protein 1
ALAS1 5'-aminolevulinate synthase 1
ALAS2 5'-aminolevulinate synthase 2
ALDH18A1 aldehyde dehydrogenase 18 family, member A1
ALDH1B1 aldehyde dehydrogenase 1 family, member B1
ALDH2 aldehyde dehydrogenase 2 family (mitochondrial)
ALDH3A2 aldehyde dehydrogenase 3 family, member A2
ALDH4A1 aldehyde dehydrogenase 4 family, member A1
ALDH5A1 aldehyde dehydrogenase 5 family, member A1
ALDH6A1 aldehyde dehydrogenase 6 family, member A1
ALDH7A1 aldehyde dehydrogenase 7 family, member A1
ALKBH7 alkB, alkylation repair homolog 7 (E. coli)
AMBRA1 autophagy/beclin-1 regulator 1
ANXA1 annexin A1
APEX2 APEX nuclease (apurinic/apyrimidinic endonuclease) 2
APOOL apolipoprotein O-like
ARG2 arginase 2
ARL2 ADP-ribosylation factor-like 2
ARL2BP ADP-ribosylation factor-like 2 binding protein
ARMCX3 armadillo repeat containing, X-linked 3
ASS1 argininosuccinate synthase 1
ATAD3A ATPase family, AAA domain containing 3A
ATAD3B ATPase family, AAA domain containing 3B
ATCAY ataxia, cerebellar, Cayman type
ATF2 activating transcription factor 2
ATG14 autophagy related 14
ATG4D autophagy related 4D, cysteine peptidase
ATG5 autophagy related 5
ATP5A1 ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle
ATP5B ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide
ATP5C1 ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1
ATP5D ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit
ATP5E ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit
ATP5F1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1
ATP5G1 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9)
ATP5G2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9)
ATP5G3 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9)
ATP5H ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d
ATP5I ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E
ATP5J ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6
ATP5J2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2
ATP5L ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G
ATP5L2 ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G2
ATP5O ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit
ATP5S ATP synthase, H+ transporting, mitochondrial Fo complex, subunit s (factor B)
ATPIF1 ATPase inhibitory factor 1
ATXN3 ataxin 3
ATXN3L ataxin 3-like
AUH AU RNA binding protein/enoyl-CoA hydratase
AURKAIP1 aurora kinase A interacting protein 1
BAD BCL2-associated agonist of cell death
BAK1 BCL2-antagonist/killer 1
BAX BCL2-associated X protein
BCAT2 branched chain amino-acid transaminase 2, mitochondrial
BCKDHA branched chain keto acid dehydrogenase E1, alpha polypeptide
BCKDHB branched chain keto acid dehydrogenase E1, beta polypeptide
BCKDK branched chain ketoacid dehydrogenase kinase
BCL2 B-cell CLL/lymphoma 2
BCL2A1 BCL2-related protein A1
BCL2L1 BCL2-like 1
BCL2L10 BCL2-like 10 (apoptosis facilitator)
BCL2L11 BCL2-like 11 (apoptosis facilitator)
BCL2L13 BCL2-like 13 (apoptosis facilitator)
BCL2L2 BCL2-like 2
BCO2 beta-carotene oxygenase 2
BCS1L BC1 (ubiquinol-cytochrome c reductase) synthesis-like
BDH1 3-hydroxybutyrate dehydrogenase, type 1
BDNF brain-derived neurotrophic factor
BID BH3 interacting domain death agonist
BIK BCL2-interacting killer (apoptosis-inducing)
BLOC1S1 biogenesis of lysosomal organelles complex-1, subunit 1
BMF Bcl2 modifying factor
BNIP3 BCL2/adenovirus E1B 19kDa interacting protein 3
BNIP3L BCL2/adenovirus E1B 19kDa interacting protein 3-like
BOK BCL2-related ovarian killer
BRI3BP BRI3 binding protein
BTD biotinidase
C10ORF2 chromosome 10 open reading frame 2
C14ORF2 chromosome 14 open reading frame 2
C19ORF12 chromosome 19 open reading frame 12
C1QBP complement component 1, q subcomponent binding protein
C9ORF89 chromosome 9 open reading frame 89
CA5A carbonic anhydrase VA, mitochondrial
CA5B carbonic anhydrase VB, mitochondrial
CABS1 calcium-binding protein, spermatid-specific 1
CANX calnexin
CARS2 cysteinyl-tRNA synthetase 2, mitochondrial (putative)
CASP8 caspase 8, apoptosis-related cysteine peptidase
CASQ1 calsequestrin 1 (fast-twitch, skeletal muscle)
CAT catalase
CBR4 carbonyl reductase 4
CCAR2 cell cycle and apoptosis regulator 2
CCDC109B coiled-coil domain containing 109B
CDS2 CDP-diacylglycerol synthase (phosphatidate cytidylyltransferase) 2
CEP89 centrosomal protein 89kDa
CHCHD1 coiled-coil-helix-coiled-coil-helix domain containing 1
CHCHD10 coiled-coil-helix-coiled-coil-helix domain containing 10
CHCHD3 coiled-coil-helix-coiled-coil-helix domain containing 3
CHCHD4 coiled-coil-helix-coiled-coil-helix domain containing 4
CHCHD5 coiled-coil-helix-coiled-coil-helix domain containing 5
CHCHD6 coiled-coil-helix-coiled-coil-helix domain containing 6
CHCHD7 coiled-coil-helix-coiled-coil-helix domain containing 7
CHDH choline dehydrogenase
CHPF chondroitin polymerizing factor
CIAPIN1 cytokine induced apoptosis inhibitor 1
CIDEA cell death-inducing DFFA-like effector a
CISD1 CDGSH iron sulfur domain 1
CISD2 CDGSH iron sulfur domain 2
CKMT2 creatine kinase, mitochondrial 2 (sarcomeric)
CLPP caseinolytic mitochondrial matrix peptidase proteolytic subunit
CLPX caseinolytic mitochondrial matrix peptidase chaperone subunit
CLU clusterin
CNP 2',3'-cyclic nucleotide 3' phosphodiesterase
COA1 cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)
COA3 cytochrome c oxidase assembly factor 3
COA7 cytochrome c oxidase assembly factor 7 (putative)
COASY CoA synthase
COQ10A coenzyme Q10 homolog A (S. cerevisiae)
COQ10B coenzyme Q10 homolog B (S. cerevisiae)
COQ2 coenzyme Q2 4-hydroxybenzoate polyprenyltransferase
COQ3 coenzyme Q3 methyltransferase
COQ4 coenzyme Q4
COQ7 coenzyme Q7 homolog, ubiquinone (yeast)
COX1
COX10 COX10 heme A:farnesyltransferase cytochrome c oxidase assembly factor
COX11 COX11 cytochrome c oxidase copper chaperone
COX14 COX14 cytochrome c oxidase assembly factor
COX15 cytochrome c oxidase assembly homolog 15 (yeast)
COX16 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
COX17 COX17 cytochrome c oxidase copper chaperone
COX18 COX18 cytochrome c oxidase assembly factor
COX19 COX19 cytochrome c oxidase assembly factor
COX2
COX20 COX20 cytochrome c oxidase assembly factor
COX3
COX4I1 cytochrome c oxidase subunit IV isoform 1
COX4I2 cytochrome c oxidase subunit IV isoform 2 (lung)
COX5A cytochrome c oxidase subunit Va
COX5B cytochrome c oxidase subunit Vb
COX6A1 cytochrome c oxidase subunit VIa polypeptide 1
COX6A2 cytochrome c oxidase subunit VIa polypeptide 2
COX6B1 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
COX6B2 cytochrome c oxidase subunit VIb polypeptide 2 (testis)
COX6C cytochrome c oxidase subunit VIc
COX7A1 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle)
COX7A2 cytochrome c oxidase subunit VIIa polypeptide 2 (liver)
COX7A2L cytochrome c oxidase subunit VIIa polypeptide 2 like
COX7B cytochrome c oxidase subunit VIIb
COX7B2 cytochrome c oxidase subunit VIIb2
COX7C cytochrome c oxidase subunit VIIc
COX8A cytochrome c oxidase subunit VIIIA (ubiquitous)
COX8C cytochrome c oxidase subunit VIIIC
CPOX coproporphyrinogen oxidase
CPS1 carbamoyl-phosphate synthase 1, mitochondrial
CPT1A carnitine palmitoyltransferase 1A (liver)
CPT1B carnitine palmitoyltransferase 1B (muscle)
CPT1C carnitine palmitoyltransferase 1C
CPT2 carnitine palmitoyltransferase 2
CRAT carnitine O-acetyltransferase
CRLS1 cardiolipin synthase 1
CS citrate synthase
CSDE1 cold shock domain containing E1, RNA-binding
CYB5A cytochrome b5 type A (microsomal)
CYB5B cytochrome b5 type B (outer mitochondrial membrane)
CYB5R3 cytochrome b5 reductase 3
CYC1 cytochrome c-1
CYCS cytochrome c, somatic
CYP11A1 cytochrome P450, family 11, subfamily A, polypeptide 1
CYP11B1 cytochrome P450, family 11, subfamily B, polypeptide 1
CYP11B2 cytochrome P450, family 11, subfamily B, polypeptide 2
CYP24A1 cytochrome P450, family 24, subfamily A, polypeptide 1
CYP27A1 cytochrome P450, family 27, subfamily A, polypeptide 1
CYP27B1 cytochrome P450, family 27, subfamily B, polypeptide 1
D2HGDH D-2-hydroxyglutarate dehydrogenase
DAO D-amino-acid oxidase
DAP3 death associated protein 3
DARS2 aspartyl-tRNA synthetase 2, mitochondrial
DBT dihydrolipoamide branched chain transacylase E2
DDX28 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28
DDX3X DEAD (Asp-Glu-Ala-Asp) box helicase 3, X-linked
DECR1 2,4-dienoyl CoA reductase 1, mitochondrial
DGUOK deoxyguanosine kinase
DHFRL1 dihydrofolate reductase-like 1
DHODH dihydroorotate dehydrogenase (quinone)
DHRS1 dehydrogenase/reductase (SDR family) member 1
DHRS2 dehydrogenase/reductase (SDR family) member 2
DHX30 DEAH (Asp-Glu-Ala-His) box helicase 30
DIABLO diablo, IAP-binding mitochondrial protein
DLAT dihydrolipoamide S-acetyltransferase
DLD dihydrolipoamide dehydrogenase
DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
DMGDH dimethylglycine dehydrogenase
DMPK dystrophia myotonica-protein kinase
DNA2 DNA replication helicase/nuclease 2
DNAJA3 DnaJ (Hsp40) homolog, subfamily A, member 3
DNAJC11 DnaJ (Hsp40) homolog, subfamily C, member 11
DNAJC15 DnaJ (Hsp40) homolog, subfamily C, member 15
DNAJC19 DnaJ (Hsp40) homolog, subfamily C, member 19
DNM1L dynamin 1-like
DTYMK deoxythymidylate kinase (thymidylate kinase)
DUSP21 dual specificity phosphatase 21
EARS2 glutamyl-tRNA synthetase 2, mitochondrial
ECHS1 enoyl CoA hydratase, short chain, 1, mitochondrial
ECI1 enoyl-CoA delta isomerase 1
EFHD1 EF-hand domain family, member D1
EPHA4 EPH receptor A4
ERAL1 Era-like 12S mitochondrial rRNA chaperone 1
ERBB4 erb-b2 receptor tyrosine kinase 4
ETFA electron-transfer-flavoprotein, alpha polypeptide
ETFB electron-transfer-flavoprotein, beta polypeptide
ETFDH electron-transferring-flavoprotein dehydrogenase
ETHE1 ethylmalonic encephalopathy 1
EXOG endo/exonuclease (5'-3'), endonuclease G-like
FAHD1 fumarylacetoacetate hydrolase domain containing 1
FARS2 phenylalanyl-tRNA synthetase 2, mitochondrial
FBXL4 F-box and leucine-rich repeat protein 4
FDX1 ferredoxin 1
FDX1L ferredoxin 1-like
FDXR ferredoxin reductase
FECH ferrochelatase
FGR FGR proto-oncogene, Src family tyrosine kinase
FH fumarate hydratase
FIS1 fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae)
FKBP8 FK506 binding protein 8, 38kDa
FLAD1 flavin adenine dinucleotide synthetase 1
FLVCR1 feline leukemia virus subgroup C cellular receptor 1
FNDC1 fibronectin type III domain containing 1
FPGS folylpolyglutamate synthase
FUNDC1 FUN14 domain containing 1
FUNDC2 FUN14 domain containing 2
FXN frataxin
GADD45GIP1 growth arrest and DNA-damage-inducible, gamma interacting protein 1
GARS glycyl-tRNA synthetase
GATM glycine amidinotransferase (L-arginine:glycine amidinotransferase)
GCDH glutaryl-CoA dehydrogenase
GDAP1 ganglioside induced differentiation associated protein 1
GFER growth factor, augmenter of liver regeneration
GFM1 G elongation factor, mitochondrial 1
GFM2 G elongation factor, mitochondrial 2
GHITM growth hormone inducible transmembrane protein
GIMAP5 GTPase, IMAP family member 5
GJA1 gap junction protein, alpha 1, 43kDa
GK glycerol kinase
GK2 glycerol kinase 2
GLS glutaminase
GLS2 glutaminase 2 (liver, mitochondrial)
GLUD1 glutamate dehydrogenase 1
GLYAT glycine-N-acyltransferase
GOLPH3 golgi phosphoprotein 3 (coat-protein)
GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial
GPAM glycerol-3-phosphate acyltransferase, mitochondrial
GPAT2 glycerol-3-phosphate acyltransferase 2, mitochondrial
GPD2 glycerol-3-phosphate dehydrogenase 2 (mitochondrial)
GPER1 G protein-coupled estrogen receptor 1
GPT2 glutamic pyruvate transaminase (alanine aminotransferase) 2
GPX1 glutathione peroxidase 1
GRAMD4 GRAM domain containing 4
GRPEL1 GrpE-like 1, mitochondrial (E. coli)
GRPEL2 GrpE-like 2, mitochondrial (E. coli)
GRSF1 G-rich RNA sequence binding factor 1
GSR glutathione reductase
GSTK1 glutathione S-transferase kappa 1
GUF1 GUF1 GTPase homolog (S. cerevisiae)
HAAO 3-hydroxyanthranilate 3,4-dioxygenase
HADH hydroxyacyl-CoA dehydrogenase
HADHA hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit
HADHB hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit
HAGH hydroxyacylglutathione hydrolase
HARS2 histidyl-tRNA synthetase 2, mitochondrial
HCCS holocytochrome c synthase
HERC2 HECT and RLD domain containing E3 ubiquitin protein ligase 2
HIBADH 3-hydroxyisobutyrate dehydrogenase
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
HIGD1A HIG1 hypoxia inducible domain family, member 1A
HIGD2A HIG1 hypoxia inducible domain family, member 2A
HK1 hexokinase 1
HK2 hexokinase 2
HMGCL 3-hydroxymethyl-3-methylglutaryl-CoA lyase
HMGCS2 3-hydroxy-3-methylglutaryl-CoA synthase 2 (mitochondrial)
HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10
HSD17B8 hydroxysteroid (17-beta) dehydrogenase 8
HSD3B1 hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 1
HSD3B2 hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2
HSPA1L heat shock 70kDa protein 1-like
HSPA9 heat shock 70kDa protein 9 (mortalin)
HSPD1 heat shock 60kDa protein 1 (chaperonin)
HSPE1 heat shock 10kDa protein 1
HTRA2 HtrA serine peptidase 2
IARS2 isoleucyl-tRNA synthetase 2, mitochondrial
IBA57 IBA57, iron-sulfur cluster assembly homolog (S. cerevisiae)
ICT1 immature colon carcinoma transcript 1
IDH2 isocitrate dehydrogenase 2 (NADP+), mitochondrial
IDH3A isocitrate dehydrogenase 3 (NAD+) alpha
IDH3B isocitrate dehydrogenase 3 (NAD+) beta
IDH3G isocitrate dehydrogenase 3 (NAD+) gamma
IFI27 interferon, alpha-inducible protein 27
IKBKE inhibitor of kappa light polypeptide gene enhancer in B-cells, kinase epsilon
IMMP1L IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae)
IMMP2L IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae)
IMMT inner membrane protein, mitochondrial
ISCU iron-sulfur cluster assembly enzyme
IVD isovaleryl-CoA dehydrogenase
KARS lysyl-tRNA synthetase
KMO kynurenine 3-monooxygenase (kynurenine 3-hydroxylase)
L2HGDH L-2-hydroxyglutarate dehydrogenase
LARS2 leucyl-tRNA synthetase 2, mitochondrial
LDHD lactate dehydrogenase D
LETM1 leucine zipper-EF-hand containing transmembrane protein 1
LETM2 leucine zipper-EF-hand containing transmembrane protein 2
LETMD1 LETM1 domain containing 1
LGALS3 lectin, galactoside-binding, soluble, 3
LONP1 lon peptidase 1, mitochondrial
LPIN1 lipin 1
LRPPRC leucine-rich pentatricopeptide repeat containing
LRRC59 leucine rich repeat containing 59
LRRK2 leucine-rich repeat kinase 2
LYN LYN proto-oncogene, Src family tyrosine kinase
LYRM4 LYR motif containing 4
LYRM7 LYR motif containing 7
MALSU1 mitochondrial assembly of ribosomal large subunit 1
MAOA monoamine oxidase A
MAOB monoamine oxidase B
MAPK8IP1 mitogen-activated protein kinase 8 interacting protein 1
MARC1 mitochondrial amidoxime reducing component 1
MARC2 mitochondrial amidoxime reducing component 2
MARCH5 membrane-associated ring finger (C3HC4) 5
MARS2 methionyl-tRNA synthetase 2, mitochondrial
MAVS mitochondrial antiviral signaling protein
MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha)
MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta)
MCEE methylmalonyl CoA epimerase
MCL1 myeloid cell leukemia 1
MCU mitochondrial calcium uniporter
MCUR1 mitochondrial calcium uniporter regulator 1
MDH2 malate dehydrogenase 2, NAD (mitochondrial)
ME2 malic enzyme 2, NAD(+)-dependent, mitochondrial
ME3 malic enzyme 3, NADP(+)-dependent, mitochondrial
METTL20 methyltransferase like 20
MFF mitochondrial fission factor
MFN1 mitofusin 1
MFN2 mitofusin 2
MGARP mitochondria-localized glutamic acid-rich protein
MGST1 microsomal glutathione S-transferase 1
MICU1 mitochondrial calcium uptake 1
MICU2 mitochondrial calcium uptake 2
MIEF1 mitochondrial elongation factor 1
MIEF2 mitochondrial elongation factor 2
MINOS1 mitochondrial inner membrane organizing system 1
MIPEP mitochondrial intermediate peptidase
MLXIP MLX interacting protein
MLYCD malonyl-CoA decarboxylase
MMAA methylmalonic aciduria (cobalamin deficiency) cblA type
MMAB methylmalonic aciduria (cobalamin deficiency) cblB type
MOAP1 modulator of apoptosis 1
MPC1 mitochondrial pyruvate carrier 1
MPC1L mitochondrial pyruvate carrier 1-like
MPC2 mitochondrial pyruvate carrier 2
MPG N-methylpurine-DNA glycosylase
MPST mercaptopyruvate sulfurtransferase
MPV17 MpV17 mitochondrial inner membrane protein
MPV17L2 MPV17 mitochondrial membrane protein-like 2
MRPL1 mitochondrial ribosomal protein L1
MRPL10 mitochondrial ribosomal protein L10
MRPL11 mitochondrial ribosomal protein L11
MRPL12 mitochondrial ribosomal protein L12
MRPL13 mitochondrial ribosomal protein L13
MRPL14 mitochondrial ribosomal protein L14
MRPL15 mitochondrial ribosomal protein L15
MRPL16 mitochondrial ribosomal protein L16
MRPL17 mitochondrial ribosomal protein L17
MRPL18 mitochondrial ribosomal protein L18
MRPL19 mitochondrial ribosomal protein L19
MRPL2 mitochondrial ribosomal protein L2
MRPL20 mitochondrial ribosomal protein L20
MRPL21 mitochondrial ribosomal protein L21
MRPL22 mitochondrial ribosomal protein L22
MRPL23 mitochondrial ribosomal protein L23
MRPL24 mitochondrial ribosomal protein L24
MRPL27 mitochondrial ribosomal protein L27
MRPL28 mitochondrial ribosomal protein L28
MRPL3 mitochondrial ribosomal protein L3
MRPL30 mitochondrial ribosomal protein L30
MRPL32 mitochondrial ribosomal protein L32
MRPL33 mitochondrial ribosomal protein L33
MRPL34 mitochondrial ribosomal protein L34
MRPL35 mitochondrial ribosomal protein L35
MRPL36 mitochondrial ribosomal protein L36
MRPL37 mitochondrial ribosomal protein L37
MRPL38 mitochondrial ribosomal protein L38
MRPL39 mitochondrial ribosomal protein L39
MRPL4 mitochondrial ribosomal protein L4
MRPL40 mitochondrial ribosomal protein L40
MRPL41 mitochondrial ribosomal protein L41
MRPL42 mitochondrial ribosomal protein L42
MRPL43 mitochondrial ribosomal protein L43
MRPL44 mitochondrial ribosomal protein L44
MRPL46 mitochondrial ribosomal protein L46
MRPL47 mitochondrial ribosomal protein L47
MRPL48 mitochondrial ribosomal protein L48
MRPL49 mitochondrial ribosomal protein L49
MRPL50 mitochondrial ribosomal protein L50
MRPL51 mitochondrial ribosomal protein L51
MRPL52 mitochondrial ribosomal protein L52
MRPL53 mitochondrial ribosomal protein L53
MRPL54 mitochondrial ribosomal protein L54
MRPL55 mitochondrial ribosomal protein L55
MRPL57 mitochondrial ribosomal protein L57
MRPL9 mitochondrial ribosomal protein L9
MRPS10 mitochondrial ribosomal protein S10
MRPS11 mitochondrial ribosomal protein S11
MRPS12 mitochondrial ribosomal protein S12
MRPS14 mitochondrial ribosomal protein S14
MRPS15 mitochondrial ribosomal protein S15
MRPS16 mitochondrial ribosomal protein S16
MRPS17 mitochondrial ribosomal protein S17
MRPS18A mitochondrial ribosomal protein S18A
MRPS18B mitochondrial ribosomal protein S18B
MRPS18C mitochondrial ribosomal protein S18C
MRPS2 mitochondrial ribosomal protein S2
MRPS21 mitochondrial ribosomal protein S21
MRPS22 mitochondrial ribosomal protein S22
MRPS23 mitochondrial ribosomal protein S23
MRPS24 mitochondrial ribosomal protein S24
MRPS25 mitochondrial ribosomal protein S25
MRPS26 mitochondrial ribosomal protein S26
MRPS27 mitochondrial ribosomal protein S27
MRPS28 mitochondrial ribosomal protein S28
MRPS30 mitochondrial ribosomal protein S30
MRPS31 mitochondrial ribosomal protein S31
MRPS33 mitochondrial ribosomal protein S33
MRPS34 mitochondrial ribosomal protein S34
MRPS35 mitochondrial ribosomal protein S35
MRPS36 mitochondrial ribosomal protein S36
MRPS5 mitochondrial ribosomal protein S5
MRPS6 mitochondrial ribosomal protein S6
MRPS7 mitochondrial ribosomal protein S7
MRPS9 mitochondrial ribosomal protein S9
MRRF mitochondrial ribosome recycling factor
MRS2 MRS2 magnesium transporter
MSTO1 misato 1, mitochondrial distribution and morphology regulator
MT-ATP6 ATP synthase F0 subunit 6
MT-ATP8 ATP synthase F0 subunit 8
MT-CYB cytochrome b
MT-ND2 MTND2
MT-ND3 NADH dehydrogenase, subunit 3 (complex I)
MT-ND4 NADH dehydrogenase, subunit 4 (complex I)
MT-ND4L NADH dehydrogenase, subunit 4L (complex I)
MT-ND5 NADH dehydrogenase, subunit 5 (complex I)
MT-ND6 NADH dehydrogenase, subunit 6 (complex I)
MTCH1 mitochondrial carrier 1
MTCH2 mitochondrial carrier 2
MTERF1 mitochondrial transcription termination factor 1
MTERF2 mitochondrial transcription termination factor 2
MTERF4 mitochondrial transcription termination factor 4
MTFP1 mitochondrial fission process 1
MTG1 mitochondrial ribosome-associated GTPase 1
MTG2 mitochondrial ribosome-associated GTPase 2
MTHFD2L methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2-like
MTOR mechanistic target of rapamycin (serine/threonine kinase)
MTRF1L mitochondrial translational release factor 1-like
MTX1 metaxin 1
MTX2 metaxin 2
MTX3 metaxin 3
MUL1 mitochondrial E3 ubiquitin protein ligase 1
MUT methylmalonyl CoA mutase
MYO19 myosin XIX
MYOC myocilin, trabecular meshwork inducible glucocorticoid response
NAGS N-acetylglutamate synthase
NARS2 asparaginyl-tRNA synthetase 2, mitochondrial (putative)
NAT8L N-acetyltransferase 8-like (GCN5-related, putative)
ND1
NDUFA1 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa
NDUFA10 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa
NDUFA11 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa
NDUFA12 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12
NDUFA13 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13
NDUFA2 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa
NDUFA3 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa
NDUFA4 NDUFA4, mitochondrial complex associated
NDUFA5 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5
NDUFA6 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa
NDUFA7 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa
NDUFA8 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa
NDUFA9 NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa
NDUFAB1 NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa
NDUFAF1 NADH dehydrogenase (ubiquinone) complex I, assembly factor 1
NDUFAF3 NADH dehydrogenase (ubiquinone) complex I, assembly factor 3
NDUFAF4 NADH dehydrogenase (ubiquinone) complex I, assembly factor 4
NDUFAF5 NADH dehydrogenase (ubiquinone) complex I, assembly factor 5
NDUFAF6 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6
NDUFB1 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa
NDUFB10 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa
NDUFB11 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa
NDUFB2 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa
NDUFB3 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa
NDUFB4 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa
NDUFB5 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa
NDUFB6 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa
NDUFB7 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa
NDUFB8 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa
NDUFB9 NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa
NDUFC1 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa
NDUFC2 NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa
NDUFC2-KCTD14 NDUFC2-KCTD14 readthrough
NDUFS1 NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)
NDUFS2 NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)
NDUFS3 NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)
NDUFS4 NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)
NDUFS5 NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)
NDUFS6 NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)
NDUFS7 NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)
NDUFS8 NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)
NDUFV1 NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa
NDUFV2 NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa
NDUFV3 NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa
NFS1 NFS1 cysteine desulfurase
NIPSNAP1 nipsnap homolog 1 (C. elegans)
NLN neurolysin (metallopeptidase M3 family)
NLRX1 NLR family member X1
NME4 NME/NM23 nucleoside diphosphate kinase 4
NNT nicotinamide nucleotide transhydrogenase
NOA1 nitric oxide associated 1
NR3C1 nuclear receptor subfamily 3, group C, member 1 (glucocorticoid receptor)
NSUN4 NOP2/Sun domain family, member 4
NT5M 5',3'-nucleotidase, mitochondrial
NUDT1 nudix (nucleoside diphosphate linked moiety X)-type motif 1
NUDT9 nudix (nucleoside diphosphate linked moiety X)-type motif 9
OAT ornithine aminotransferase
OCIAD2 OCIA domain containing 2
OGDH oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
OGDHL oxoglutarate dehydrogenase-like
OMA1 OMA1 zinc metallopeptidase
OPA1 optic atrophy 1 (autosomal dominant)
OTC ornithine carbamoyltransferase
OXA1L oxidase (cytochrome c) assembly 1-like
OXCT1 3-oxoacid CoA transferase 1
PABPC5 poly(A) binding protein, cytoplasmic 5
PAM16 presequence translocase-associated motor 16 homolog (S. cerevisiae)
PANK2 pantothenate kinase 2
PARG poly (ADP-ribose) glycohydrolase
PARK7 parkinson protein 7
PARL presenilin associated, rhomboid-like
PARS2 prolyl-tRNA synthetase 2, mitochondrial (putative)
PC pyruvate carboxylase
PCCA propionyl CoA carboxylase, alpha polypeptide
PCCB propionyl CoA carboxylase, beta polypeptide
PCK2 phosphoenolpyruvate carboxykinase 2 (mitochondrial)
PDE12 phosphodiesterase 12
PDE2A phosphodiesterase 2A, cGMP-stimulated
PDHA1 pyruvate dehydrogenase (lipoamide) alpha 1
PDHA2 pyruvate dehydrogenase (lipoamide) alpha 2
PDHB pyruvate dehydrogenase (lipoamide) beta
PDHX pyruvate dehydrogenase complex, component X
PDK1 pyruvate dehydrogenase kinase, isozyme 1
PDK2 pyruvate dehydrogenase kinase, isozyme 2
PDK3 pyruvate dehydrogenase kinase, isozyme 3
PDK4 pyruvate dehydrogenase kinase, isozyme 4
PDP1 pyruvate dehyrogenase phosphatase catalytic subunit 1
PDP2 pyruvate dehyrogenase phosphatase catalytic subunit 2
PDPR pyruvate dehydrogenase phosphatase regulatory subunit
PDSS1 prenyl (decaprenyl) diphosphate synthase, subunit 1
PDSS2 prenyl (decaprenyl) diphosphate synthase, subunit 2
PEMT phosphatidylethanolamine N-methyltransferase
PGAM5 phosphoglycerate mutase family member 5
PGR progesterone receptor
PGS1 phosphatidylglycerophosphate synthase 1
PHB prohibitin
PHB2 prohibitin 2
PI4KB phosphatidylinositol 4-kinase, catalytic, beta
PIN4 peptidylprolyl cis/trans isomerase, NIMA-interacting 4
PINK1 PTEN induced putative kinase 1
PITRM1 pitrilysin metallopeptidase 1
PLA2G4A phospholipase A2, group IVA (cytosolic, calcium-dependent)
PLD6 phospholipase D family, member 6
PLN phospholamban
PLSCR3 phospholipid scramblase 3
PMAIP1 phorbol-12-myristate-13-acetate-induced protein 1
PMPCA peptidase (mitochondrial processing) alpha
PMPCB peptidase (mitochondrial processing) beta
PNPLA7 patatin-like phospholipase domain containing 7
PNPT1 polyribonucleotide nucleotidyltransferase 1
POLDIP2 polymerase (DNA-directed), delta interacting protein 2
POLG polymerase (DNA directed), gamma
POLG2 polymerase (DNA directed), gamma 2, accessory subunit
POLRMT polymerase (RNA) mitochondrial (DNA directed)
POP7 processing of precursor 7, ribonuclease P/MRP subunit (S. cerevisiae)
PPA2 pyrophosphatase (inorganic) 2
PPIF peptidylprolyl isomerase F
PPM1K protein phosphatase, Mg2+/Mn2+ dependent, 1K
PPOX protoporphyrinogen oxidase
PPP1R15A protein phosphatase 1, regulatory subunit 15A
PPP2R2B protein phosphatase 2, regulatory subunit B, beta
PRDX1 peroxiredoxin 1
PRDX3 peroxiredoxin 3
PRDX5 peroxiredoxin 5
PRELID1 PRELI domain containing 1
PRELID2 PRELI domain containing 2
PRIMPOL primase and polymerase (DNA-directed)
PRKCA protein kinase C, alpha
PRODH proline dehydrogenase (oxidase) 1
PRODH2 proline dehydrogenase (oxidase) 2
PSEN1 presenilin 1
PSEN2 presenilin 2
PTCD1 pentatricopeptide repeat domain 1
PTCD3 pentatricopeptide repeat domain 3
PTPMT1 protein tyrosine phosphatase, mitochondrial 1
PYCR1 pyrroline-5-carboxylate reductase 1
QARS glutaminyl-tRNA synthetase
RAB11FIP5 RAB11 family interacting protein 5 (class I)
RAD51 RAD51 recombinase
RAF1 Raf-1 proto-oncogene, serine/threonine kinase
RARS2 arginyl-tRNA synthetase 2, mitochondrial
RDH13 retinol dehydrogenase 13 (all-trans/9-cis)
REEP1 receptor accessory protein 1
REXO2 RNA exonuclease 2
RHOT1 ras homolog family member T1
RHOT2 ras homolog family member T2
RMDN3 regulator of microtubule dynamics 3
RNF144B ring finger protein 144B
RNF185 ring finger protein 185
RNF5 ring finger protein 5, E3 ubiquitin protein ligase
ROMO1 reactive oxygen species modulator 1
RPS3 ribosomal protein S3
RPS6KB1 ribosomal protein S6 kinase, 70kDa, polypeptide 1
RSAD2 radical S-adenosyl methionine domain containing 2
SAMM50 SAMM50 sorting and assembly machinery component
SARDH sarcosine dehydrogenase
SARM1 sterile alpha and TIR motif containing 1
SARS2 seryl-tRNA synthetase 2, mitochondrial
SCO1 SCO1 cytochrome c oxidase assembly protein
SCO2 SCO2 cytochrome c oxidase assembly protein
SDHA succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
SDHAF1 succinate dehydrogenase complex assembly factor 1
SDHAF2 succinate dehydrogenase complex assembly factor 2
SDHAF3 succinate dehydrogenase complex assembly factor 3
SDHAF4 succinate dehydrogenase complex assembly factor 4
SDHB succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
SDHC succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
SDHD succinate dehydrogenase complex, subunit D, integral membrane protein
SFXN1 sideroflexin 1
SFXN2 sideroflexin 2
SFXN3 sideroflexin 3
SFXN4 sideroflexin 4
SFXN5 sideroflexin 5
SH3GLB1 SH3-domain GRB2-like endophilin B1
SHC1 SHC (Src homology 2 domain containing) transforming protein 1
SHMT2 serine hydroxymethyltransferase 2 (mitochondrial)
SIRT3 sirtuin 3
SIRT4 sirtuin 4
SIRT5 sirtuin 5
SLC11A2 solute carrier family 11 (proton-coupled divalent metal ion transporter), member 2
SLC25A1 solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1
SLC25A10 solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10
SLC25A11 solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11
SLC25A12 solute carrier family 25 (aspartate/glutamate carrier), member 12
SLC25A13 solute carrier family 25 (aspartate/glutamate carrier), member 13
SLC25A14 solute carrier family 25 (mitochondrial carrier, brain), member 14
SLC25A15 solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15
SLC25A16 solute carrier family 25 (mitochondrial carrier), member 16
SLC25A18 solute carrier family 25 (glutamate carrier), member 18
SLC25A19 solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19
SLC25A2 solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 2
SLC25A20 solute carrier family 25 (carnitine/acylcarnitine translocase), member 20
SLC25A21 solute carrier family 25 (mitochondrial oxoadipate carrier), member 21
SLC25A22 solute carrier family 25 (mitochondrial carrier: glutamate), member 22
SLC25A23 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 23
SLC25A24 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 24
SLC25A25 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 25
SLC25A26 solute carrier family 25 (S-adenosylmethionine carrier), member 26
SLC25A27 solute carrier family 25, member 27
SLC25A28 solute carrier family 25 (mitochondrial iron transporter), member 28
SLC25A29 solute carrier family 25 (mitochondrial carnitine/acylcarnitine carrier), member 29
SLC25A3 solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3
SLC25A30 solute carrier family 25, member 30
SLC25A31 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 31
SLC25A32 solute carrier family 25 (mitochondrial folate carrier), member 32
SLC25A33 solute carrier family 25 (pyrimidine nucleotide carrier), member 33
SLC25A34 solute carrier family 25, member 34
SLC25A35 solute carrier family 25, member 35
SLC25A36 solute carrier family 25 (pyrimidine nucleotide carrier), member 36
SLC25A37 solute carrier family 25 (mitochondrial iron transporter), member 37
SLC25A38 solute carrier family 25, member 38
SLC25A39 solute carrier family 25, member 39
SLC25A4 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4
SLC25A40 solute carrier family 25, member 40
SLC25A41 solute carrier family 25, member 41
SLC25A42 solute carrier family 25, member 42
SLC25A43 solute carrier family 25, member 43
SLC25A44 solute carrier family 25, member 44
SLC25A45 solute carrier family 25, member 45
SLC25A46 solute carrier family 25, member 46
SLC25A47 solute carrier family 25, member 47
SLC25A48 solute carrier family 25, member 48
SLC25A5 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5
SLC25A51 solute carrier family 25, member 51
SLC25A52 solute carrier family 25, member 52
SLC25A53 solute carrier family 25, member 53
SLC25A6 solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6
SLC27A3 solute carrier family 27 (fatty acid transporter), member 3
SLC3A1 solute carrier family 3 (amino acid transporter heavy chain), member 1
SLC44A1 solute carrier family 44 (choline transporter), member 1
SLC8B1 solute carrier family 8 (sodium/lithium/calcium exchanger), member B1
SLC9B2 solute carrier family 9, subfamily B (NHA2, cation proton antiporter 2), member 2
SLMO1 slowmo homolog 1 (Drosophila)
SLMO2 slowmo homolog 2 (Drosophila)
SMCP sperm mitochondria-associated cysteine-rich protein
SMDT1 single-pass membrane protein with aspartate-rich tail 1
SNCA synuclein, alpha (non A4 component of amyloid precursor)
SNN stannin
SNPH syntaphilin
SOD1 superoxide dismutase 1, soluble
SOD2 superoxide dismutase 2, mitochondrial
SORD sorbitol dehydrogenase
SOX10 SRY (sex determining region Y)-box 10
SPATA18 spermatogenesis associated 18
SPATA19 spermatogenesis associated 19
SPG20 spastic paraplegia 20 (Troyer syndrome)
SPG7 spastic paraplegia 7 (pure and complicated autosomal recessive)
SPNS1 spinster homolog 1 (Drosophila)
SQRDL sulfide quinone reductase-like (yeast)
SRC SRC proto-oncogene, non-receptor tyrosine kinase
SSBP1 single-stranded DNA binding protein 1, mitochondrial
ST20 suppressor of tumorigenicity 20
STAR steroidogenic acute regulatory protein
STARD13 StAR-related lipid transfer (START) domain containing 13
STAT3 signal transducer and activator of transcription 3 (acute-phase response factor)
STOML2 stomatin (EPB72)-like 2
STX17 syntaxin 17
SUCLA2 succinate-CoA ligase, ADP-forming, beta subunit
SUCLG1 succinate-CoA ligase, alpha subunit
SUCLG2 succinate-CoA ligase, GDP-forming, beta subunit
SUOX sulfite oxidase
SUPV3L1 suppressor of var1, 3-like 1 (S. cerevisiae)
SURF1 surfeit 1
SYNJ2BP synaptojanin 2 binding protein
TAMM41 TAM41, mitochondrial translocator assembly and maintenance protein, homolog (S. cerevisiae)
TARS2 threonyl-tRNA synthetase 2, mitochondrial (putative)
TAZ tafazzin
TDRD7 tudor domain containing 7
TEFM transcription elongation factor, mitochondrial
TERT telomerase reverse transcriptase
TFAM transcription factor A, mitochondrial
TFB1M transcription factor B1, mitochondrial
TFB2M transcription factor B2, mitochondrial
THEM4 thioesterase superfamily member 4
THEM5 thioesterase superfamily member 5
TIMM10 translocase of inner mitochondrial membrane 10 homolog (yeast)
TIMM10B translocase of inner mitochondrial membrane 10 homolog B (yeast)
TIMM13 translocase of inner mitochondrial membrane 13 homolog (yeast)
TIMM17A translocase of inner mitochondrial membrane 17 homolog A (yeast)
TIMM17B translocase of inner mitochondrial membrane 17 homolog B (yeast)
TIMM21 translocase of inner mitochondrial membrane 21 homolog (yeast)
TIMM22 translocase of inner mitochondrial membrane 22 homolog (yeast)
TIMM23 translocase of inner mitochondrial membrane 23 homolog (yeast)
TIMM44 translocase of inner mitochondrial membrane 44 homolog (yeast)
TIMM50 translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
TIMM8A translocase of inner mitochondrial membrane 8 homolog A (yeast)
TIMM8B translocase of inner mitochondrial membrane 8 homolog B (yeast)
TIMM9 translocase of inner mitochondrial membrane 9 homolog (yeast)
TIMMDC1 translocase of inner mitochondrial membrane domain containing 1
TK2 thymidine kinase 2, mitochondrial
TMEM11 transmembrane protein 11
TMEM126A transmembrane protein 126A
TMEM126B transmembrane protein 126B
TMEM14C transmembrane protein 14C
TMEM173 transmembrane protein 173
TMEM70 transmembrane protein 70
TMLHE trimethyllysine hydroxylase, epsilon
TOMM20 translocase of outer mitochondrial membrane 20 homolog (yeast)
TOMM20L translocase of outer mitochondrial membrane 20 homolog (yeast)-like
TOMM22 translocase of outer mitochondrial membrane 22 homolog (yeast)
TOMM34 translocase of outer mitochondrial membrane 34
TOMM40 translocase of outer mitochondrial membrane 40 homolog (yeast)
TOMM40L translocase of outer mitochondrial membrane 40 homolog (yeast)-like
TOMM5 translocase of outer mitochondrial membrane 5 homolog (yeast)
TOMM6 translocase of outer mitochondrial membrane 6 homolog (yeast)
TOMM7 translocase of outer mitochondrial membrane 7 homolog (yeast)
TOMM70A translocase of outer mitochondrial membrane 70 homolog A (S. cerevisiae)
TOP1MT topoisomerase (DNA) I, mitochondrial
TP53 tumor protein p53
TRAP1 TNF receptor-associated protein 1
TRIAP1 TP53 regulated inhibitor of apoptosis 1
TRMT10C tRNA methyltransferase 10 homolog C (S. cerevisiae)
TRMT5 tRNA methyltransferase 5
TSPO translocator protein (18kDa)
TST thiosulfate sulfurtransferase (rhodanese)
TTC19 tetratricopeptide repeat domain 19
TUFM Tu translation elongation factor, mitochondrial
TXN2 thioredoxin 2
TXNIP thioredoxin interacting protein
TXNRD2 thioredoxin reductase 2
TYMS thymidylate synthetase
UBIAD1 UbiA prenyltransferase domain containing 1
UCP1 uncoupling protein 1 (mitochondrial, proton carrier)
UCP2 uncoupling protein 2 (mitochondrial, proton carrier)
UCP3 uncoupling protein 3 (mitochondrial, proton carrier)
UQCC1 ubiquinol-cytochrome c reductase complex assembly factor 1
UQCC2 ubiquinol-cytochrome c reductase complex assembly factor 2
UQCC3 ubiquinol-cytochrome c reductase complex assembly factor 3
UQCR10 ubiquinol-cytochrome c reductase, complex III subunit X
UQCR11 ubiquinol-cytochrome c reductase, complex III subunit XI
UQCRB ubiquinol-cytochrome c reductase binding protein
UQCRC1 ubiquinol-cytochrome c reductase core protein I
UQCRC2 ubiquinol-cytochrome c reductase core protein II
UQCRFS1 ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1
UQCRH ubiquinol-cytochrome c reductase hinge protein
UQCRQ ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
USMG5 up-regulated during skeletal muscle growth 5 homolog (mouse)
USP30 ubiquitin specific peptidase 30
VAMP1 vesicle-associated membrane protein 1 (synaptobrevin 1)
VAT1 vesicle amine transport 1
VDAC1 voltage-dependent anion channel 1
VDAC2 voltage-dependent anion channel 2
VDAC3 voltage-dependent anion channel 3
VRK2 vaccinia related kinase 2
WARS2 tryptophanyl tRNA synthetase 2, mitochondrial
YARS2 tyrosyl-tRNA synthetase 2, mitochondrial
YME1L1 YME1-like 1 ATPase
ZFYVE1 zinc finger, FYVE domain containing 1