Metabolism of amino acids and derivatives Gene Set

Dataset Reactome Pathways
Category structural or functional annotations
Type pathway
External Link http://www.reactome.org/PathwayBrowser/#/R-HSA-71291
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Genes

188 proteins participating in the Metabolism of amino acids and derivatives pathway from the Reactome Pathways dataset.

Symbol Name
AADAT aminoadipate aminotransferase
AANAT aralkylamine N-acetyltransferase
AASS aminoadipate-semialdehyde synthase
ACAD8 acyl-CoA dehydrogenase family, member 8
ACADSB acyl-CoA dehydrogenase, short/branched chain
ACAT1 acetyl-CoA acetyltransferase 1
ACMSD aminocarboxymuconate semialdehyde decarboxylase
ADI1 acireductone dioxygenase 1
AFMID arylformamidase
AGMAT agmatine ureohydrolase (agmatinase)
AGXT alanine-glyoxylate aminotransferase
AGXT2 alanine--glyoxylate aminotransferase 2
AHCY adenosylhomocysteinase
ALDH18A1 aldehyde dehydrogenase 18 family, member A1
ALDH4A1 aldehyde dehydrogenase 4 family, member A1
ALDH6A1 aldehyde dehydrogenase 6 family, member A1
ALDH7A1 aldehyde dehydrogenase 7 family, member A1
ALDH9A1 aldehyde dehydrogenase 9 family, member A1
AMD1 adenosylmethionine decarboxylase 1
AMDHD1 amidohydrolase domain containing 1
APIP APAF1 interacting protein
ARG1 arginase 1
ARG2 arginase 2
ASL argininosuccinate lyase
ASMT acetylserotonin O-methyltransferase
ASNS asparagine synthetase (glutamine-hydrolyzing)
ASS1 argininosuccinate synthase 1
AUH AU RNA binding protein/enoyl-CoA hydratase
AZIN1 antizyme inhibitor 1
AZIN2 antizyme inhibitor 2
BBOX1 butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
BCAT1 branched chain amino-acid transaminase 1, cytosolic
BCAT2 branched chain amino-acid transaminase 2, mitochondrial
BCKDHA branched chain keto acid dehydrogenase E1, alpha polypeptide
BCKDHB branched chain keto acid dehydrogenase E1, beta polypeptide
BHMT betaine--homocysteine S-methyltransferase
CBS cystathionine-beta-synthase
CCBL1 cysteine conjugate-beta lyase, cytoplasmic
CCBL2 cysteine conjugate-beta lyase 2
CDO1 cysteine dioxygenase type 1
CGA glycoprotein hormones, alpha polypeptide
CKB creatine kinase, brain
CKM creatine kinase, muscle
CKMT1A creatine kinase, mitochondrial 1A
CKMT2 creatine kinase, mitochondrial 2 (sarcomeric)
CNDP2 CNDP dipeptidase 2 (metallopeptidase M20 family)
CPS1 carbamoyl-phosphate synthase 1, mitochondrial
CSAD cysteine sulfinic acid decarboxylase
CTH cystathionine gamma-lyase
DAO D-amino-acid oxidase
DBH dopamine beta-hydroxylase (dopamine beta-monooxygenase)
DBT dihydrolipoamide branched chain transacylase E2
DDC dopa decarboxylase (aromatic L-amino acid decarboxylase)
DIO1 deiodinase, iodothyronine, type I
DIO2 deiodinase, iodothyronine, type II
DIO3 deiodinase, iodothyronine, type III
DLD dihydrolipoamide dehydrogenase
DLST dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
ENOPH1 enolase-phosphatase 1
ETHE1 ethylmalonic encephalopathy 1
FAH fumarylacetoacetate hydrolase (fumarylacetoacetase)
FTCD formimidoyltransferase cyclodeaminase
GAMT guanidinoacetate N-methyltransferase
GATM glycine amidinotransferase (L-arginine:glycine amidinotransferase)
GCDH glutaryl-CoA dehydrogenase
GCLC glutamate-cysteine ligase, catalytic subunit
GCLM glutamate-cysteine ligase, modifier subunit
GLS glutaminase
GLS2 glutaminase 2 (liver, mitochondrial)
GLUD1 glutamate dehydrogenase 1
GLUL glutamate-ammonia ligase
GOT1 glutamic-oxaloacetic transaminase 1, soluble
GOT2 glutamic-oxaloacetic transaminase 2, mitochondrial
GPT glutamic-pyruvate transaminase (alanine aminotransferase)
GPT2 glutamic pyruvate transaminase (alanine aminotransferase) 2
GRHPR glyoxylate reductase/hydroxypyruvate reductase
GSTZ1 glutathione S-transferase zeta 1
HAAO 3-hydroxyanthranilate 3,4-dioxygenase
HAL histidine ammonia-lyase
HAO1 hydroxyacid oxidase (glycolate oxidase) 1
HDC histidine decarboxylase
HGD homogentisate 1,2-dioxygenase
HIBADH 3-hydroxyisobutyrate dehydrogenase
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
HPD 4-hydroxyphenylpyruvate dioxygenase
HSD17B10 hydroxysteroid (17-beta) dehydrogenase 10
IDO1 indoleamine 2,3-dioxygenase 1
IDO2 indoleamine 2,3-dioxygenase 2
IVD isovaleryl-CoA dehydrogenase
IYD iodotyrosine deiodinase
KMO kynurenine 3-monooxygenase (kynurenine 3-hydroxylase)
KYNU kynureninase
MAT1A methionine adenosyltransferase I, alpha
MCCC1 methylcrotonoyl-CoA carboxylase 1 (alpha)
MCCC2 methylcrotonoyl-CoA carboxylase 2 (beta)
MRI1 methylthioribose-1-phosphate isomerase 1
MTAP methylthioadenosine phosphorylase
MTR 5-methyltetrahydrofolate-homocysteine methyltransferase
MTRR 5-methyltetrahydrofolate-homocysteine methyltransferase reductase
NAGS N-acetylglutamate synthase
NQO1 NAD(P)H dehydrogenase, quinone 1
OAT ornithine aminotransferase
OAZ1 ornithine decarboxylase antizyme 1
OAZ2 ornithine decarboxylase antizyme 2
OAZ3 ornithine decarboxylase antizyme 3
ODC1 ornithine decarboxylase 1
OGDH oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
OTC ornithine carbamoyltransferase
PAH phenylalanine hydroxylase
PAOX polyamine oxidase (exo-N4-amino)
PCBD1 pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha
PHGDH phosphoglycerate dehydrogenase
PNMT phenylethanolamine N-methyltransferase
PRODH proline dehydrogenase (oxidase) 1
PSAT1 phosphoserine aminotransferase 1
PSMA1 proteasome (prosome, macropain) subunit, alpha type, 1
PSMA2 proteasome (prosome, macropain) subunit, alpha type, 2
PSMA3 proteasome (prosome, macropain) subunit, alpha type, 3
PSMA4 proteasome (prosome, macropain) subunit, alpha type, 4
PSMA5 proteasome (prosome, macropain) subunit, alpha type, 5
PSMA6 proteasome (prosome, macropain) subunit, alpha type, 6
PSMA7 proteasome (prosome, macropain) subunit, alpha type, 7
PSMA8 proteasome (prosome, macropain) subunit, alpha type, 8
PSMB1 proteasome (prosome, macropain) subunit, beta type, 1
PSMB10 proteasome (prosome, macropain) subunit, beta type, 10
PSMB11 proteasome (prosome, macropain) subunit, beta type, 11
PSMB2 proteasome (prosome, macropain) subunit, beta type, 2
PSMB3 proteasome (prosome, macropain) subunit, beta type, 3
PSMB4 proteasome (prosome, macropain) subunit, beta type, 4
PSMB5 proteasome (prosome, macropain) subunit, beta type, 5
PSMB6 proteasome (prosome, macropain) subunit, beta type, 6
PSMB7 proteasome (prosome, macropain) subunit, beta type, 7
PSMB8 proteasome (prosome, macropain) subunit, beta type, 8
PSMB9 proteasome (prosome, macropain) subunit, beta type, 9
PSMC1 proteasome (prosome, macropain) 26S subunit, ATPase, 1
PSMC2 proteasome (prosome, macropain) 26S subunit, ATPase, 2
PSMC3 proteasome (prosome, macropain) 26S subunit, ATPase, 3
PSMC4 proteasome (prosome, macropain) 26S subunit, ATPase, 4
PSMC5 proteasome (prosome, macropain) 26S subunit, ATPase, 5
PSMC6 proteasome (prosome, macropain) 26S subunit, ATPase, 6
PSMD1 proteasome (prosome, macropain) 26S subunit, non-ATPase, 1
PSMD10 proteasome (prosome, macropain) 26S subunit, non-ATPase, 10
PSMD11 proteasome (prosome, macropain) 26S subunit, non-ATPase, 11
PSMD12 proteasome (prosome, macropain) 26S subunit, non-ATPase, 12
PSMD13 proteasome (prosome, macropain) 26S subunit, non-ATPase, 13
PSMD14 proteasome (prosome, macropain) 26S subunit, non-ATPase, 14
PSMD2 proteasome (prosome, macropain) 26S subunit, non-ATPase, 2
PSMD3 proteasome (prosome, macropain) 26S subunit, non-ATPase, 3
PSMD4 proteasome (prosome, macropain) 26S subunit, non-ATPase, 4
PSMD5 proteasome (prosome, macropain) 26S subunit, non-ATPase, 5
PSMD6 proteasome (prosome, macropain) 26S subunit, non-ATPase, 6
PSMD7 proteasome (prosome, macropain) 26S subunit, non-ATPase, 7
PSMD8 proteasome (prosome, macropain) 26S subunit, non-ATPase, 8
PSMD9 proteasome (prosome, macropain) 26S subunit, non-ATPase, 9
PSME1 proteasome (prosome, macropain) activator subunit 1 (PA28 alpha)
PSME2 proteasome (prosome, macropain) activator subunit 2 (PA28 beta)
PSME3 proteasome (prosome, macropain) activator subunit 3 (PA28 gamma; Ki)
PSME4 proteasome (prosome, macropain) activator subunit 4
PSMF1 proteasome (prosome, macropain) inhibitor subunit 1 (PI31)
PSPH phosphoserine phosphatase
PYCR1 pyrroline-5-carboxylate reductase 1
QDPR quinoid dihydropteridine reductase
SAT1 spermidine/spermine N1-acetyltransferase 1
SHMT1 serine hydroxymethyltransferase 1 (soluble)
SLC25A10 solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10
SLC25A15 solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15
SLC25A2 solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 2
SLC25A21 solute carrier family 25 (mitochondrial oxoadipate carrier), member 21
SLC5A5 solute carrier family 5 (sodium/iodide cotransporter), member 5
SLC6A11 solute carrier family 6 (neurotransmitter transporter), member 11
SLC6A12 solute carrier family 6 (neurotransmitter transporter), member 12
SLC6A7 solute carrier family 6 (neurotransmitter transporter), member 7
SLC6A8 solute carrier family 6 (neurotransmitter transporter), member 8
SMOX spermine oxidase
SMS spermine synthase
SQRDL sulfide quinone reductase-like (yeast)
SRM spermidine synthase
SUOX sulfite oxidase
TAT tyrosine aminotransferase
TDO2 tryptophan 2,3-dioxygenase
TH tyrosine hydroxylase
TMLHE trimethyllysine hydroxylase, epsilon
TPH1 tryptophan hydroxylase 1
TPH2 tryptophan hydroxylase 2
TPO thyroid peroxidase
TSHB thyroid stimulating hormone, beta
TST thiosulfate sulfurtransferase (rhodanese)
UROC1 urocanate hydratase 1